Idiopathic retroperitoneal fibrosis; Ormond's disease
Powerful anti-inflammatory medicines called corticosteroids are tried first. Some doctors also use a drug called tamoxifen to treat this condition.
If corticosteroid treatment doesn't work, a biopsy should be done to confirm the diagnosis. If confirmed, other medicines to suppress the immune system are usually prescribed.
When medicine does not work, surgery and stents (draining tubes) are needed.
Prognosis depends on the extent of the fibrosis and the amount of damage to the kidneys. The kidney damage may be temporary or permanent.
The disorder may lead to:
Call your health care provider if you experience lower abdomen or flank pain, particularly with decreased urine volume.
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