Treatment:

Early complete surgical repair is needed. In surgery, the pulmonary veins are connected to the left atrium and the defect between the right and left atrium is closed.

Expectations (prognosis):

If left untreated, death may occur by age 1 in babies with more severe defects. With surgery, early repair provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart.

Complications:

• Heart failure
• Breathing difficulties
• Lung infections
• Pulmonary hypertension
• Irregular, fast heart rhythms (arrhythmias)

Calling your health care provider:

This condition may be apparent at the time of birth. However, symptoms may not be present until later.

Call your health care provider if you notice symptoms of TAPVR -- prompt attention is required!