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Anomalous origin of the left coronary artery arising from the pulmonary artery; ALCAPA; ALCAPA syndrome; Bland-White-Garland syndrome
Surgery is needed to correct ALCAPA. Usually only one surgery is required, depending on the baby's condition and the size of the involved blood vessels.
If the heart muscle supporting the mitral valve is seriously damaged from decreased oxygen, the baby may also need surgery to repair or replace the valve. The mitral valve regulates blood flow between the chambers on the left side of the heart.
If the baby's heart is already severely damaged from lack of oxygen, a heart transplant may be an option.
Very ill babies may need treatment with medications before surgery. The medications help the baby get strong enough to have surgery.
Without treatment, most babies do not survive their first year. Those who survive without treatment are likely to have severe complications and other cardiovascular problems, or to die suddenly during the following years.
With timely treatment, most babies do well and can expect a normal life. However, they need routine follow-ups with a heart specialist (cardiologist).
Complications of ALCAPA include:
Call your health care provider if your baby:
Other Congenital Heart and Vascular Malformations. In: Kliegman RM, Behrman RE, Jenson HB, et al., eds. Nelson Textbook of Pediatrics, 18th ed. Philadelphia, Pa: Saunders Elsevier;2007:chap 432.
Marelli AJ. In: Mandell GL, Bennett JE, Dolin R. Goldman: Cecil Medicine. 23rd ed. Philadelphia, Pa: Saunders Elsevier; 2007:chap 68.
Park MK. Park: Pediatric Cardiology for Practitioners, 5th ed. Philadelphia, PA: Mosby Elsevier; 2008.
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