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Fiebre mediterránea familiar - Overview

Nombres alternativos

Poliserositis paroxística familiar; Peritonitis periódica; Poliserositis recurrente; Peritonitis paroxística benigna; Enfermedad periódica; Fiebre periódica; PPF

Definición:

Es un trastorno que se transmite de padres a hijos (hereditario) y que consiste en episodios repetitivos de fiebre e inflamación que con frecuencia afecta el revestimiento del abdomen, el tórax o las articulaciones.

Causas, incidencia y factores de riesgo:

La fiebre mediterránea familiar casi siempre es causada por una mutación en el gen MEFV. Este gen crea proteínas involucradas en la inflamación.

La enfermedad generalmente afecta a personas de ascendencia mediterránea, especialmente a los judíos que no son asquenacíes (sefardíes), armenios y árabes, aunque también puede afectar a personas de otros grupos étnicos.

La enfermedad es muy poco común y, entre los factores de riesgo, están tener antecedentes familiares de este tipo de fiebre o ancestros mediterráneos.

  • Reviewed last on: 9/15/2010
  • David C. Dugdale, III, MD, Professor of Medicine, Division of General Medicine, Department of Medicine, University of Washington School of Medicine; Jatin M. Vyas, MD, PhD, Assistant Professor in Medicine, Harvard Medical School; Assistant in Medicine, Division of Infectious Disease, Department of Medicine, Massachusetts General Hospital. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc.

Referencias

Kastner DL. The systemic autoinflammatory diseases. In: Goldman L, Ausiello D, eds. Cecil Medicine. 23rd ed. Philadelphia, Pa: Saunders Elsevier; 2007:chap 282.

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