A Member of the University of Maryland Medical System   |   In Partnership with the University of Maryland School of Medicine

Share

Email PageEmail Print PagePrint

Home > Medical Reference > Encyclopedia (English)

Toggle: English / Spanish

Síndrome de Chediak-Higashi - Treatment

Tratamiento:

No hay un tratamiento específico para el síndrome de Chediak-Higashi, aunque los trasplantes de médula ósea parecen haber tenido éxito en algunos pacientes, especialmente cuando se llevan a cabo en las etapas iniciales de la enfermedad.

Los antibióticos se utilizan para tratar las infecciones. Los medicamentos antivirales, como el aciclovir y los medicamentos quimioterapéuticos, con frecuencia se utilizan en la fase acelerada de la enfermedad. Es posible que se requiera cirugía para drenar los abscesos en algunos casos.

Grupos de apoyo:

Chediak-Higashi Syndrome Association:www.chediak-higashi.org.

Pronóstico:

La muerte suele ocurrir en los primeros 10 años de vida, debido a las infecciones crónicas o a la enfermedad acelerada que ocasiona un padecimiento similar al linfoma. Sin embargo, algunos niños afectados han sobrevivido por más tiempo.

Posibles complicaciones:

  • Infecciones frecuentes especialmente con el virus Epstein-Barr
  • Cáncer similar al linfoma
  • Muerte prematura

Cuándo contactar a un profesional médico:

Consulte con el médico si tiene antecedentes familiares de este trastorno y está planeando tener hijos.

Solicite una cita médica si su hijo muestra síntomas del síndrome de Chediak-Higashi.

  • Reviewed last on: 8/4/2011
  • Chad Haldeman-Englert, MD, Wake Forest University School of Medicine, Department of Pediatrics, Section on Medical Genetics, Winston-Salem, NC. Review provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc.

Referencias

Boxer LA. Disorders of Phagocyte Function. In: Kliegman RM, Behrman RE, Jenson HB, Stanton BF, eds. Nelson Textbook of Pediatrics. 18th Ed. Philadelphia, Pa: Saunders Elsevier; 2007: chap 129.

The information provided herein should not be used during any medical emergency or for the diagnosis or treatment of any medical condition. A licensed medical professional should be consulted for diagnosis and treatment of any and all medical conditions. Call 911 for all medical emergencies. Links to other sites are provided for information only -- they do not constitute endorsements of those other sites. © 1997- A.D.A.M., Inc. Any duplication or distribution of the information contained herein is strictly prohibited.
adam.com
Adam QualityA.D.A.M., Inc. is accredited by URAC, also known as the American Accreditation HealthCare Commission (www.urac.org). URAC's accreditation program is an independent audit to verify that A.D.A.M. follows rigorous standards of quality and accountability. A.D.A.M. is among the first to achieve this important distinction for online health information and services. Learn more about A.D.A.M.'s editorial policy, editorial process and privacy policy. A.D.A.M. is also a founding member of Hi-Ethics and subscribes to the principles of the Health on the Net Foundation (www.hon.ch).

The information provided herein should not be used during any medical emergency or for the diagnosis or treatment of any medical condition. A licensed medical professional should be consulted for diagnosis and treatment of any and all medical conditions. Call 911 for all medical emergencies. Links to other sites are provided for information only -- they do not constitute endorsements of those other sites. © 1997- A.D.A.M., Inc. Any duplication or distribution of the information contained herein is strictly prohibited.
adam.com
Connect with UMMC
Facebook Twitter YouTube Blog iPhone

Please rate the quality of this article.

Do you find this article to be helpful / informative?
              
Poor                                       Excellent

Do you have any brief comments on this page: (up to 255 characters)

© 2011 University of Maryland Medical Center (UMMC). All rights reserved.
UMMC is a member of the University of Maryland Medical System,
22 S. Greene Street, Baltimore, MD 21201. TDD: 1-800-735-2258 or 1.866.408.6885